Microcephalicosteodysplastic primordial dwarfism type 2 (MOPD 2) is a rare autosomal recessive disorder of growth restriction, short stature, skeletal abnormalities and an unusually small head size, which have their onset during intrauterine life with the fetus exhibiting intrauterine growth restriction.Affected individuals also tend to have a very small head size and termed microcephalic. The growth problems progress postnatally, causing stunted growth or short stature. In this case report, we present the case of a 5 year old girl first born of Nonconsanguineous marriage came to paediatric OPD seeking treatment for severe growth retardation since infancy.