Marfan syndrome (MFS) is a connective tissue disorder leading to multisystem abnormalities mainly skeletal, cardiovascular system and ocular manifestations. It has an autosomal dominant inheritancewhich is why familial cases occur frequently. It is caused by mutations in the fibrillin gene present on chromosome 15.1Ocular manifestations are common. These are increased axial length, decreased corneal curvature, greater corneal astigmatism, myopia, ectopia lentis and retinal detachment. The diagnosis of MFS is clinical, but genetic testing is available.2A significant proportion of the patients of the with MFS are initially seen for an ocular pathology mainly decreased vision and diagnosed by an ophthalmologist. Thus, alertness of the ophthalmologists when examining a patient with suspicious ocular findings can help in the early diagnosis. Early diagnosis and management have significantly increased the life expectancy in these patients. These patients should be examined regularly to identify potential complications.