iarmsIARMSIARMS2709-3255https://doi.org/10.47310/iarms.2020.v01i01.001Isolated Polycystic Liver Disease (PKHI)A.ElfaroukiM.A.LkousseY.IsmailJ.ElatmaniA.AiterramiS.OubahaZ.Samlani1K.KratiPKHI isolated hepatic polycystosis, first described in 1856 by Bristowe, is most often associated with autosomal dominant polycystic kidney disease to give autosomal dominant hepato-renal polycystosis. Hepatic cysts are the most common extrarenal manifestation of autosomal dominant polycystic liver disease. We report the case of a young patient diagnosed with PKHI during a chronic abdominal pain assessment.