iarjmcrIARJMCRIARJMCR2709-3220https://doi.org/10.47310/iarjmcr.2022.v03i01.017Focal Cortical Dysplasia with Underlying Dysembryoplastic Neuroepithelial Tumor: A Case ReportAshwiniNagdaPoorviAgrawalPoonamWadeDepartment of Pediatrics, Topiwala National Medical College and B.Y.L. Nair Charitable Hospital, Mumbai Central, 400008, Mumbai, Maharashtra, IndiaEpilepsy associated with slow growing brain tumors may frequently be the cause for pharmacoresistant focal seizures in young children. Dysembryoplastic neuroepithelial tumor is one such entity which may cause epilepsy resistant to multiple antiepileptic agents. Focal cortical dysplasia, a congenital cortical developmental anomaly which may be seen associated with DNET, independently acts as an epileptogenic focus. Early diagnosis of such lesions is necessary. Long term use of antiepileptic drugs (AEDs), needed for control of tumor related epilepsy and might affect the cognitive development of the child. Complete surgical removal of the tumor along with overlying dysplasia is one of the modalities for making the patient seizure free. However, the risks of surgery and neurological development post-surgery should also be considered while deciding on the management of LEATs in pediatric patients.