iarjmcrIARJMCRIARJMCR2709-3220https://doi.org/10.47310/iarjmcr.2021.v02i01.016Ewing's sarcoma of the temporal bone: case report of a child and review of the literatureFadwaAlloucheFzTerrabHKabbajFFarhaneZAlamiTBouhafaKHassouniEwing's sarcoma is the second most common primary bone malignancy in children after osteosarcoma. It represents 4 to 9% of primary malignant bone tumors and affects the bones of the skull (maxillary, frontal, parietal, ethmoid, temporal bones) in only 1 to 4% of cases. Therefore, it rarely affects the head and neck. In this case report, we describe a case of a 13-year-old boy with left temporal Ewing sarcoma. When this patient presented with left temporal swelling and headache, imaging studies showed a mixed mass originating from the left temporal bone. During the biopsy and surgery (incomplete resection), the mass was invaded the facial nerve, which then required a nerve transplant. Postoperatively, he then underwent radiotherapy with induction and adjuvant chemotherapy. Although it is a rare tumor of the temporal bone, physicians should consider Ewing's sarcoma in the differential diagnosis of children and adolescents with facial nerve palsy. With a generally poor prognosis due to early metastasis to the lungs and other bones.